Infantile amaurotic idiocy $(Tay-Sachs disease)$ is

• A

  The result of severe protein deficiency in diet and damages the muscle development in growing children

• B

  An inherited disorder in which the spinal cord and brain are severely damaged within a few months of birth leading to paralysis and mental retardation, and finally the infant's death in $3$ or $4$ years

• C

  A genetic abnormality which appears at the age of $25-30$ years and damages the bones

• D

  A chromosomal disorder in young children